Optimising Dietary Management in Inborn Errors of Metabolism: Implications for Brain Development

This presentation by Dr. Kevin Strauss, Medical Director at the Clinic for Special Children, Strasburg, PA from Global Nutricia Metabolics Expert Day, 2024, titled 'Optimising dietary management in inborn errors of metabolism: implications for brain development' delves into the topic of brain amino acid metabolism in IMDs. 
Key topics include:
  • Relationship between plasma levels and brain uptake of essential amino acids, an overview of how these processes are interconnected. 
  • The impact of medical food composition on brain amino acid nutrition and development, particularly in the context of disorders of intermediary metabolism. 
By exploring these topics, the talk aims to shed light on the critical role that amino acids play in brain health and development, and how dietary interventions can influence these outcomes. 
optimising-dietary-management-in-inborn-errors-of-metabolism-implications-for-brain-development

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